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ABDOMEN / Peritoneum mesentery   42 / F,  Abdominal pain
2024-08-30
About Author
Authors Youe Ree Kim
Institution Wonkwang University Hospital
E-mail sweetynn@naver.com
About Case
Chief complaint
or Title
Abdominal pain
Subspecialty ABDOMEN / Peritoneum mesentery
Classification Neoplasm, benign / fibrous
Age 42 Sex F
Difficulty For resident, For specialist
Modality CT
Case Figures
Click above Figure for more images.
Questions
What causes intestinal obstruction? What is your diagnosis?
Answer
Diagnosis Desmoid tumor (fibromatosis)
Comments
The patient was diagnosed with familial adenomatous polyposis several years ago and underwent total colectomy with ileal pouch anastomosis. A few years later, intestinal obstruction occurred,a CT scan was performed, revealing an infiltrative mass at the anastomosis site. Differential diagnoses included desmoid tumor (fibromatosis), actinomycosis, inflammatory pseudotumor, and rectal cancer infiltration. Desmoid tumor (fibromatosis) was diagnosed after ultrasound-guided biopsy.













References 1.Shinagare AB, Ramaiya NH, Jagannathan JP et al. A to Z of desmoid tumors. AJR Am J Roentgenol. 2011 Dec;197(6):W1008-14. doi: 10.2214/AJR.11.6657. PMID: 22109314.
2. Braschi-Amirfarzan M, Keraliya AR, Krajewski KM et al. Role of Imaging in Management of Desmoid-type Fibromatosis: A Primer for Radiologists. Radiographics. 2016 May-Jun;36(3):767-82. doi: 10.1148/rg.2016150153. PMID: 27163593.
Keywords Fibromatosis, Fibrosis, Desmoid tumor, FAP
Attachment File -

Number of Applicants : 23
Correct Answer 5
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