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ABDOMEN / Hepatobiliary   79 / M,  Abdominal pain
2022-05-27
About Author
Authors Sunyoung Lee
Institution Severance Hospital, Yonsei University College of Medicine
E-mail carnival0126@gmail.com
About Case
Chief complaint
or Title
Abdominal pain
Subspecialty ABDOMEN / Hepatobiliary
Classification Neoplasm, Malignancy / others
Age 79 Sex M
Difficulty For resident, For specialist
Modality CT, MR
Case Figures
Click above Figure for more images.
Questions
What is a diagnosis?
Answer
Diagnosis Angiosarcoma
Comments

Hepatic angiosarcoma





¡×Accounts
for 2% of primary hepatic tumors


¡×Most
common malignant mesenchymal tumor of the liver


¡×Commonly
affects patients 60-70 years of age


¡×Strong
male predominance (M:F = 4:1)


¡×Most patients have metastatic
lesions at the time of presentation (site: lung > spleen)


¡×Poor
prognosis (most patients die < 1 year)


¡×Can
appear as


1)Multiple
hypoattenuating nodules
(foci of enhancement may be present)


2)Dominant
masses with heterogeneous internal architecture in T2 MR (similar to
HCC)


- heterogeneous
and progressive enhancement



3)Diffusely
infiltrating lesion


¡×Hematologic
abnormalities are often accompanied


¡×Microangiopathic
hemolytic anemia


¡×Thrombocytopenia


¡×Disseminated
intravascular coagulation



References
Keywords Angiosarcoma
Attachment File -

Number of Applicants : 47
Correct Answer 16
Shiga University of Medical Science Akitoshi Inoue
Jichi Medical University School of Medicine Mitsuru Matsuki
Juntendo University Moto Nakaya
The University of Tokyo Toshihiro Furuta
Kyoto University Hospital Yasuhisa Kurata
Kyoto University Hospital Yusuke Utsunomiya
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