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ABDOMEN / Abdomen general   43 / M,  What disease you can find?
About Author
Authors shin yong moon
Institution Asan Medical Center
E-mail cjimage@amc.seoul.kr
About Case
Chief complaint
or Title		 What disease you can find?
Subspecialty ABDOMEN / Abdomen general
Classification systemic disease / others
Age 43 Sex M
Difficulty For student, For resident
Modality CT, MR, Etc
Case Figures
Click above Figure for more images.
Questions
Answer
Diagnosis 4 Pancreas IPMN
Comments




 

 

 

 


Von Hippel-Lindau Syndrome


= Inherited neurocutaneous dysplasia complex


Involving organs


  1. CNS :


  1. Hemangioblastoma : Cerebellum, spine

  2. Retina : angiomatosis ( - 45%)


  1. Kidney


  1. Cortical renal cyst( 75%)

  2. Renal cell Carcinoma ( 28-45%)

  3. Renal adenoma

  4. Renal hemangioma


  1. Epipidymis


  1. Cystadenoma


  1. Adrenal Gland


  1. Pheochromocytoma ( 17%)


  1. Pancreas


  1. Cystadenoma

  2. Neuroendocrine tumor

  3. Hemangioblastoma

  4. Pancreas cyst ( 30%), usually multiple


  1. Liver


  1. Hemangioma

  2. Adenoma


  1. Others


  1. Paraganglioma

  2. Hemangioblastoma


 
References
Keywords Von Hippel Lindau, Pancreas, Renal cell carcinoma
Attachment File -

Number of Applicants : 34
Correct Answer 15
Higashi-Ohmi General Medical Center Akitoshi Inoue
University of Tokyo Hospital Toshihiro Furuta
군의관 김동환
한림대성심병원 김민정
서울대학교병원 김보람
서울대병원 김세형
세브란스병원 김연윤
고대구로병원 김정우
중앙보훈병원 김주원
순천향대학교 부천병원 변성환
서울의료원 안태란
서울시보라매병원 우현식
서울아산병원 이경진
고대안암병원 이동규
경북대학교병원 임춘근
Semi-Correct Answer 5
명지병원 김경호
세브란스 병원 김동규
중앙보훈병원 김윤이
서울아산병원 장종건
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